Congenital self-healing reticulohistiocytosis

Congenital self-healing reticulohistiocytosis

Congenital self-healing reticulohistiocytosis (also known as "Hashimoto–Pritzker disease,"[1] and "Hashimoto–Pritzker syndrome"[2]) is a condition that is a self-limited form of Langerhans cell histiocytosis.[2]:720

Symptoms

Non-specific inflammatory response, which includes fever, lethargy, and weight loss. This is suspected of being a genetic disorder, and as the name implies, is self healing.

  • Skin: Commonly seen are a rash which varies from scaly erythematous lesions to red papules pronounced in intertriginous areas. Up to 80% of patients have extensive eruptions on the scalp.
  • Lymph node: Enlargement of the lymph nodes in 50% of Histiocytosis cases.[3]

History

It was first described by Ken Hashimoto and M. S. Pritzkar in 1973.[4][5]

See also

References

  1. ↑ Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 1-4160-2999-0.
  2. 1 2 James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 0-7216-2921-0.
  3. ↑ "Langerhans Cell Histiocytosis - Patient UK". Retrieved 2007-05-10.
  4. ↑ John Thorne Crissey; Lawrence C. Parish; Karl Holubar (2013). Historical Atlas of Dermatology and Dermatologists. CRC Press. p. 179. ISBN 1-84214-100-7.
  5. ↑ Lee, Young H.; Talekar, Mala K.; Chung, Catherine G.; Bell, Moshe D.; Zaenglein, Andrea L. (February 2014). "Congenital Self-Healing Reticulohistiocytosis". The Journal of Clinical and Aesthetic Dermatology. 7 (2): 49–53. ISSN 1941-2789. PMC 3935651. PMID 24578781.
Classification
External resources


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